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fa Enlarged follicles and temporomandibular joint abnormalities in mucolipidosis Type III رادیولوژی دهان، فک و صورت Oral and Maxillofacial Radiology گزارش مورد case report Mucolipidosis Type III, or pseudo-Hurler polydystrophy, is a rare genetic abnormality, the result of a mutation to one of two genes that encode the hexameric protein N-acetylglucosaminyl-1-phosphotransferase (Glc-NAc-PT). The abnormality results in the accumulation of unprocessed macromolecules in cell and tissue compartments throughout the body. In this case report, we describe the clinical and radiographic findings of a 15-year-old male with this disorder. He presented with bilateral ectopically developing mandibular molar teeth with enlarged follicles and multiple joint involvement, including the temporomandibular joints. The patient underwent surgical removal of the molar teeth and curettage of the associated follicles. The subsequent histopathological examination of the tissues revealed hyperplastic follicles suggestive of dentigerous cysts. This report presents the plain film and cone beam CT examinations of the patient. <hr> Source: DentoMaxilloFacial Radiology <a href="http://dmfr.birjournals.org/content/42/4/22822014.abstract" target="_blank">Full Text</a> mucolipidosis Type III ,temporomandibular joint ,impacted teeth 0 0 http://idai.ir/browse.php?a_code=A-10-32-1385&slc_lang=fa&sid=1 H Khalifa 10031947532846006338 10031947532846006338 No Discipline of Oral and Maxillofacial Radiology, Faculty of Dentistry, University of Toronto, Toronto, ON, Canada HS Grubisa 10031947532846006339 10031947532846006339 No Private Practice in Orthodontics, Toronto, ON, Canada L Lee 10031947532846006340 10031947532846006340 No Department of Dentistry, Princess Margaret Hospital, Toronto, ON, Canada EWN Lam ernest.lam@dentistry.utoronto.ca 10031947532846006341 10031947532846006341 Yes Discipline of Oral and Maxillofacial Radiology, Faculty of Dentistry, University of Toronto, Toronto, ON, Canada